Korean Journal of Thoracic and Cardiovascular Surgery 2018; 51(6): 419-422  https://doi.org/10.5090/kjtcs.2018.51.6.419
An Aggressive Large Epithelioid Hemangioendothelioma of the Anterior Mediastinum in a Young Woman
Roman Dutta1, Harish Pal2, Garima Garg3, and Sambit Mohanty3
1Department of Thoracic Surgery, Nayati Medicity, Departments of 2General and Minimal Access Surgery and 3Pathology, Max Super Speciality Hospital
Corresponding author: Harish Pal, Department of General and Minimal Access Surgery, Max Super Speciality Hospital, W-3, Vaishali Sector 1, Delhi-NCR, 201012, India
(Tel) 91-0120-4173000 (Fax) 91-1204173010 (E-mail) drharishpal007@gmail.com
Received: August 23, 2018; Revised: October 3, 2018; Accepted: October 16, 2018.; Published online: December 5, 2018.
© The Korean Journal of Thoracic and Cardiovascular Surgery. All rights reserved.

cc This is an open access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
Abstract
Hemangioendothelioma is a rare vascular tumor with involvement of the liver, brain, long bones, and lung. Among the 6 histological subtypes, epithelioid hemangioendothelioma (EHE) is the most aggressive. Its occurrence in the mediastinum is quite rare, and very few cases have been documented. The reported cases in the literature have described difficulties in the preoperative diagnosis due to the unusual histological appearance of the tumor. Immunohistochemistry remains the mainstay for a definitive diagnosis. Due to its low incidence, there is no standard treatment for mediastinal EHE, but curative resection is the preferred treatment option where possible, with chemotherapy used as an adjuvant treatment or in cases of widespread inoperable disease. The present case study describes an aggressive EHE occurring in an 18 year-old woman in the anterior mediastinum.
Keywords: Hemangioendothelioma, Mediastinum, Vascular neoplasms


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