Korean J Thorac Cardiovasc Surg 2019; 52(2): 100-104  https://doi.org/10.5090/kjtcs.2019.52.2.100
Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient
Beatrice Chia-Hui Shih , M.D., Jae Hong Lim , M.D., Jooncheol Min , M.D., Eung Re Kim , M.D., Jae Gun Kwak , M.D., Ph.D., Woong-Han Kim , M.D., Ph.D.
Department of Pediatric Thoracic and Cardiovascular Surgery, Seoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, Korea
Corresponding author: Woong-Han Kim, Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine, 101 Daehak-ro, Jongno-gu, Seoul 03080, Korea,
(Tel) 82-2-2072-3637 (Fax) 82-2-3672-3637 (E-mail) woonghan@snu.ac.kr
Received: August 1, 2018; Revised: November 30, 2018; Accepted: December 3, 2018.; Published online: April 5, 2019.
© The Korean Journal of Thoracic and Cardiovascular Surgery. All rights reserved.

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Abstract
Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral valve and coarctation of the aorta who underwent successful single-stage surgical repair.
Keywords: Shone’s complex, Bicuspid aortic valve, Parachute mitral valve, Extraanatomic bypass, Aortic coarctation


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